DIAGNOSIS IN PATIENTS TRANSPLANTED WITH NCBP UNITS (9/30/06)

 

 

 

Frequency

 

Aspartylglucosaminuria

 

1

 

Adrenoleukodystrophy

 

26

 

Acute Lymphoblastic Leukemia

 

605

 

Alpha-mannosidosis

 

2

 

Acute Myelogenous Leukemia

 

529

 

Amegakaryocytic Thrombocytopenia

 

6

 

Amyloidosis

 

1

 

Acute Promyelocytic Leukemia

 

2

 

Biphenotypic Leukemia

 

7

 

Burkitt's Lymphoma

 

9

 

Breast Cancer

 

1

 

Congenital Erythropoietic Porphyria

 

1

 

Chronic Granulomatous Disease

 

5

 

Chediak-Higashi Syndrome

 

5

 

Chronic Lymphocytic Leukemia

 

14

 

Chronic Myelogenous Leukemia

 

171

 

Congenital Neutropenia

 

3

 

Congenital Thrombocytopenia

 

1

 

Common Variable Immune Deficiency

 

3

 

Diamond-Blackfan Anemia

 

13

 

DiGeorge Syndrome

 

1

 

Dyskeratosis Congenita

 

6

 

EBV Lymphoproliferative Disease

 

3

 

Fanconi Anemia

 

67

 

Familial Erythrophagocytic Lymphohistiocytosis

 

22

 

Fucosidosis

 

1

 

Gangliosidosis

 

1

 

Gaucher's Disease

 

2

 

Glanzmann's Thrombasthenia

 

2

 

Griscelli Syndrome

 

1

 

Hodgkin's Disease

 

29

 

Hemophagocytic Lymphohistiocytosis

 

18

 

Hunter's Syndrome

 

2

 

Hurler Disease

 

41

 

Hurler-Scheie Disease

 

1

 

I-cell Disease

 

4

 

Infantile Ceroid Lipofucoscinosis

 

1

 

X-linked Immune Dysregulation Polyendrocrine Enteropathy

 

2

 

Idiopathic Thrombocytopenic Purpura

 

1

 

Juvenile Chronic Myelogenous Leukemia

 

33

 

Juvenile Mono-Myelocytic Leukemia

 

13

 

Kostmann Syndrome

 

9

 

Krabbe Disease

 

20

 

Lymphocyte Adhesion Disease

 

5

 

Langerhans Cell Histiocytosis

 

8

 

Lesch-Nyhan Syndrome

 

4

 

Lupus

 

1

 

Lymphoma

 

10

 

Mantle Cell Lymphoma

 

2

 

Myelodysplasia

 

104

 

Myelofibrosis

 

1

 

Metachromatic Leukodystrophy

 

13

 

Maroteaux-Lamy Syndrome

 

6

 

Multliple Myeloma

 

6

 

Morquio Syndrome

 

1

 

Mucopolysacharidosis

 

1

 

Neuroblastoma

 

13

 

Non-Hodgkin's Lymphoma

 

53

 

Neiman-Pick Disease

 

1

 

Nezelof Syndrome

 

1

 

Omenn Syndrome

 

2

 

Osteopetrosis

 

36

 

Paroxysmal Nocturnal Hemoglobinuria

 

1

 

Reticular Dysgenesis

 

1

 

Severe Aplastic Anemia

 

72

 

Sandhoff Disease

 

1

 

Sanfilippo Disease

 

2

 

Sideroblastic Anemia

 

1

 

Sickle Cell Disease

 

10

 

Severe Combined Immune Deficiency

 

74

 

Shwachman-Diamond Syndrome

 

3

 

Sialidosis

 

1

 

Thalassemia

 

24

 

Tay Sach Disease

 

3

 

Undifferentiated Acute Leukemia

 

1

 

Wiskott-Aldrich Syndrome

 

42

 

Wolman Disease

 

2

 

X-linked HyperIgM Syndrome

 

5

 

X-linked Lymphoproliferative Disease

 

3

 

Total

 

2199

 


Hematologic Malignancies (9/30/06)

 

 

 

Frequency

 

Acute Lymphoblastic Leukemia

 

605

 

Acute Myelogenous Leukemia

 

529

 

Acute Promyelocytic Leukemia

 

2

 

Biphenotypic Leukemia

 

7

 

Burkitt's Lymphoma

 

9

 

Chronic Lymphocytic Leukemia

 

14

 

Chronic Myelogenous Leukemia

 

171

 

EBV Lymphoproliferative Disease

 

3

 

Hodgkin's Disease

 

29

 

Juvenile Chronic Myelogenous Leukemia

 

33

 

Juvenile Mono-Myelocytic Leukemia

 

13

 

Lymphoma